Table 2

Summary of the clinical outcomes of the cases of sclerosing epithelioid fibrosarcoma reported in the literature

Series/Case reportPatients with follow upDuration of follow upNo evidence of disease (%; duration)Recurrence (%; time from Dx)Metastasis (%; time from Dx)Death (%; time from Dx)
AWD, alive with disease; Dx, diagnosis; NA, not available.
Meis-Kindblom et al (1995)11613–207 months6/16 (37%; 13–204 months)8/15 (53%; 28–132 months)6/14 (43%; 56–168 months)4/16 (25%; 37–164 months)
Reid et al (1996)2196 months (AWD)001 (60 months)0
Christensen et al (1997)3NANANANANANA
Eyden et al (1998)444–84 months2/4 (50%; 4–36 months)2/4 (50%; 10–24 months)1/4 (25%; not stated)1/4 (25%; 84 months)
Gisselsson et al (1998)5124 months (AWD)01 (24 months)00
Donner et al (2000)6114 months1 (14 months)000
Bilsky et al (2000)7312–59 months0/3 (0%)2/3 (67%; 10–13 months)3/3 (100%; 0–36 months)1/3 (33%; 59 months)
Arya et al (2001)8148 months1 (48 months)000
Antonescu et al (2001)91413–124 months1/14 (7%; 13 months)7/14 (50%; 2–46 months)12/14 (86%; 0–102 months)8/14 (57%; 13–86 months)
Hanson et al (2001)10112 months001 (1.5 months)1 (12 months)
Jiao et al (2002)11120 months1 (20 months)000
Abdulkader et al (2002)12160 months001 (36 months)0
Cumulative data444–207 months12/43 (28%; 13–204 months)20/42 (48%; 2–132 months)25/42 (60%; 0–168 months)15/43 (35%; 12–164 months)