Table 1

 Clinical findings of the 16 ES/PNETs

CaseAge (years)SexTumour siteTumour size (cm)RT-PCRFISHFollow up (months)Outcome
*Decalcified tissue was used.
AWD, alive with disease; CDF, continued disease free; DOD, died of disease; ES/PNET, Ewing’s sarcoma and primitive neuroectodermal tumour; FISH, fluorescence in situ hybridisation; NA, data not available; ND, not detected; RT-PCR, reverse transcription polymerase chain reaction.
111MFemur10.0EWS–FLI1Positive32DOD
215MThigh16.0NDPositive11DOD
318FRib4.0EWS–FLI1ND*56CDF
419MThigh8.0EWS–FLI1Positive75CDF
528MKidneyNANAPositiveNANA
628FHumerus9.0NDND*6CDF
731FRetroperitoneum6.0NAPositive10DOD
832FDuodenum6.0NAPositive24DOD
937FPancreasNANAPositiveNANA
1043FSacrum7.5NAPositive3AWD
1152MEpiduraNAEWS–FLI1PositiveNANA
1256FRetroperitoneumNANAPositiveNANA
1357FChest wall6.0NAPositive4AWD
1460FThigh4.1EWS–FLI1Positive8CDF
1561FKidneyNANAPositiveNANA
1672FRetroperitoneum5.0NAPositive3AWD