Table 1

Clinical characteristics of 10 patients with marginal zone B cell lymphoma with IgG4-positive plasma cells

Patient no.Age (years)/genderLateralityClinical stage*Initial treatmentEvents during follow-upSecond treatmentOutcome and follow-up (months)
166/MBilateralT2cN4M0/IIIRadiationMalignant transformation to diffuse large cell typeCHOP and rituximabDied from disease (36)
266/MLeftT2cN0M0/IERadiationOrbital LPI; gastric LPIrituximabAOD (97)
367/FLeftT2cN0M0/IERadiationGastric carcinoma and LPI, developing TNM staging N4Gastrectomy, CHOP and rituximabAOD (70)
475/MLeftT2cN0M0/IERadiationDeveloping TNM staging N4NDDied from other cause (65)
564/FLeftT2bN0M0/IECPDeveloping TNM staging N3NDAWD (82)
670/MRightT2cN4M0/IIIExcisionNoneNDAWD (13)
761/MLeftT2cN0M0/IERadiationDeveloping TNM staging N4NDAWD (73)
890/MLeftT2cN4M0/IIIRadiationNoneNDAOD (9)
965/MRightT2bN0M0/IERadiationNoneNDAOD (26)
1064/MRightT2cN0M0/IERadiationNoneNDAOD (26)
  • * American Joint Committee on Cancer staging and Ann Arbor staging.

  • AOD, alive without disease; AWD, alive with disease; CHOP, cyclophosphamide, doxorubicin, vincristine, prednisone; LPI, lymphoplasmacytic infiltrations; TNM, tumour, node, metastases.