No of cases | Splenomegaly | Hepatomegaly | Pancytopenia | Circulating proerythroblasts | Survival (months) | |
---|---|---|---|---|---|---|
*One case had no hepatosplenomegaly at presentation, but did have hepatic, splenic, and renal infiltration with pronormoblasts at necropsy. | ||||||
**Median of all cases with survival data (40 in total). | ||||||
ND, not determined or individually reported. | ||||||
Di Guglielmo 19282 | 1 | 1/1 | 1/1 | 1/1 | 1/1 | 2 |
Lazzaro 193315 | 1 | 1/1 | 1/1 | 0/1 | 1/1 | 0.5 |
Stodmeister 194116 | 1 | 1/1 | 1/1 | 0/1 | 1/1 | 0 |
Mirchandani et al 198317 | 1 | 0/1 | 0/1 | 1/1 | 0/1 | 3 |
Reiffers et al 198518 | 2 | 1/2* | 0/2* | 2/2 | 1/2 | 0.5, 1 |
Ruvidic iet al 19865 | 1 | ND | ND | 1/1 | 0/1 | 0.5 |
Griesser and Hornby 19876 | 11 | 0/11 | 1/11 | 11/11 | 7/11 | 0.5–4 |
Kowal-Vern et al 199219 | 13 | ND | ND | ND | ND | 0.1–9 |
Tsuji et al 199520 | 1 | 1/1 | 1/1 | 1/1 | 0/1 | 2 |
Mazzella et al 199821 | 15 | ND | ND | ND | ND | 0.5–14.5 |
Hasserjian et al 2000 | 2 | 2/2 | 1/2 | 2/2 | 1/2 | 0, 4 |
Total | 49 | 7/20 (35%) | 6/20 (30%) | 19/21 (90%) | 12/21 (57%) | 1.5** |