Specimen | Analyte | Reference range |
---|---|---|
Urinary porphyrin: creatinine ratios are higher in children weighing less than 30 kg or less than 9 years old.10 | ||
The reference range for erythrocytes refers to packed erythrocytes. | ||
Urine | Porphobilinogen | <10 μmol/l |
<1.5 μmol/mmol creatinine | ||
Total porphyrin | 20–320 nmol/l | |
<35 nmol/mmol creatinine | ||
Faeces | Total porphyrin | 10–200 nmol/g dry wt |
Erythrocytes | Total porphyrin | 0.4–1.7 μmol/l |