Table 1

Characteristics of desmoplastic small round cell tumour (DSRCT)

PatientAge at diagnosis (years)SiteStatusHistological subtypingt(11;22) (p13;q12)CCN2 expression
NED, no evidence of disease; NSE, neurone specific enolase.
115Lymph nodeDeadPositive for vimentin, desmin, NSE, and keratinNegativeNegative
210.5AbdomenDeadPositive for desmin and keratinPositivePositive
Negative for NSE and actin
315Peritoneum, omentumAlive, NEDPositive for desminPositivePositive
Negative for CD45, CD99, and actin