Table 1

Clinical and pathological data, histological diagnoses, morphology and immunohistochemical expression in the WDLPS and DDLPS cases

Case no.Sex/ageLocalisation/size (cm)DiagnosisSubtype or dedifferentiated area morphologyIHC MDM2/CDK4MDM2/CDK4 staining patternObservations
1M/65Retroperitoneum/17WDLPSLipoma-like+/+1/1Stroma with myxoid areas
2M/76Retroperitoneum/15WDLPSEsclerosing+/+2/1
4M/68Thorax/7WDLPSLipoma-like+/−1/4
5M/63Retroperitoneum/31WDLPSEsclerosing+/−1/3
9M/NIRetroperitoneum/44WDLPSEsclerosing+/−2/4
10M/59Retroperitoneum/10DDLPSUPS+/+1/1
13M/35Retroperitoneum/17DDLPSUPS+/+1/1
14M/72Cervical/BIWDLPSLipoma-like+/−1/4
16M/66Thigh/6WDLPSLipoma-like+/+1/1Hibernomatous-like cells
17F/48Retroperitoneum/25WDLPSEsclerosing+/+1/1
18M/58Retroperitoneum/19WDLPSLipoma-like+/+1/1Floret-like cells
19F/73Thigh/33DDLPSUPS−/−3/4
22F/32Leg/14WDLPSLipoma-like+/−1/4
27M/77Retroperitoneum/12WDLPSEsclerosing+/+1/1
28F/55Retroperitoneum/11DDLPSUPS+/+1/1
29F/73Retroperitoneum/24DDLPSLG-SCS+/+1/1
32NI/NIKnee/IBWDLPSEsclerosing+/+1/1
38NI/NINI/NIWDLPSEsclerosing+/+1/1
50F/49Thigh/7WDLPSLipoma-like+/−1/4
51M/58Thigh/10DDLPSUPS+/−1/4
68F/80Pelvis/22DDLPSMyx-UPS+/−1/4
70F/80Retroperitoneum/35DDLPSMXFBS-like+/+1/1
73M/65Retroperitoneum/15DDLPSUPS+/+1/1
75M/70Retroperitoneum/40WDLPSEsclerosing+/+1/1
106F/49Arm/15WDLPSLipoma-like+/+1/2
112M/56Scalp/5WDLPSEsclerosing+/+1/1
126M/54Cervical/10WDLPSSpindle cell+/+1/1Stroma with myxoid areas
127F/38Retroperitoneum/6DDLPSNeural-like nodules+/+1/1With metaplastic bone
129M/47Dorsal/7WDLPSLipoma-like+/+1/1
  • Staining pattern: 1, diffuse positivity (>30% of cells were immunoreactive); 2, moderate positivity (10–29% of cells were immunoreactive); 3, focal positivity (<10% of cells were immunoreactive); 4, negative (no cell was immunoreactive).

  • M, male; F, female; IB, incisional biopsy; NI, non-informed; WDLPS, well differentiated liposarcoma; DDLPS, dedifferentiated liposarcoma; UPS, undifferentiated pleomorphic sarcoma; LG-SCS, low grade spindle cell sarcoma; Myx-UPS, myxoid undifferentiated pleomorphic sarcoma; MXFBS, mixofibrosarcoma.