Cases | Primary, recurrence | Mean age (range) | F/M | Tumour grades I–III | L1CAM pos | NfkappaB p65 pos | YAP1 pos |
PAX6 mean % (range) | |
EPN-RELA | 10 | 5/5 | 22.5 (3–42) | 2/8 | 0-0-10 | 6/8 | 8/8 | 7/7 | 17.1 (1.9–38.3) |
EPN-YAP1 | 2 | 1/1 | 2 (1–3) | 1/1 | 0-0-2 | 0/2 | 0/2 | 1/2 | 41 (6.3–75.6) |
SE-SUP | 5 | 5/0 | 50.8 (40–66) | 2/3 | 5-0-0 | 0/5 | 0/5 | 4/5 | 6.7 (0.7–19.6) |
PFA | 16 | 9/7 | 7.5 (2–42) | 6/10 | 0-5-11 | 1/8 | 1/7 | 5/6 | 32.8 (1–95.6) |
PFB | 24 | 20/4 | 45.2 (20–77) | 11/13 | 0-17-7 | 0/23 | 0/23 | 22/23 | 29.3 (0.5–94) |
SE-INF | 5 | 5/0 | 61.6 (47–75) | 0/5 | 5-0-0 | 0/5 | 0/5 | 3/4 | 3.4 (0.7–10.7) |
MPE | 29 | 27/2 | 38.4 (9–60) | 11/18 | 29-0-0 | 0/27 | 0/28 | 18/26 | 30.9 (2.9–78.5) |
EPN-SPINE | 68 | 64/4 | 47.1 (11–82) | 33/35 | 0-63-5 | 2/65 | 2/66 | 48/59 | 31 (0.4–97.5) |
EPN-NC | 13 | 11/2 | 40,61 (2–74) | 3/10 | 0-6-7 | 0/12 | 0/12 | 3/12 | 15 (0–61.3) |
EPN-NC, not classified; EPN-RELA, ependymoma RELA-fusion positive; EPN-SPINE, spinal ependymoma; EPN-YAP1, ependymoma with Yap1 fusion; MPE, myxopapillary ependymoma; PAX6, paired box 6; PFA, posterior fossa group A ; PFB, posterior fossa group B ependymoma; SE-INF, subependymoma infratentorial; SE-SUP, subependymoma supratentorial.